What are the principles of cystic fibrosis?

What are the principles of cystic fibrosis?

Summary. We advocate for policies that promote access to the highly specialized care and treatments that a person with cystic fibrosis needs to live a long and healthy life. Principles that drive all our work include adequacy, affordability, availability, transparency, and value.

What can you teach a patient with cystic fibrosis?

Encourage your child to exercise regularly and drink lots of fluids. Your child should see their healthcare provider at least every 3 months, or as directed. Don’t let people smoke in your home, car, or anywhere near your child. Talk with your child about the dangers of smoking.

How do you care for someone with cystic fibrosis?

Antibiotics to treat and prevent lung infections. Anti-inflammatory medications to lessen swelling in the airways in your lungs. Mucus-thinning drugs, such as hypertonic saline, to help you cough up the mucus, which can improve lung function.

What protein is affected in cystic fibrosis?

Summary. Cystic fibrosis is caused by mutations in the gene that produces the cystic fibrosis transmembrane conductance regulator (CFTR) protein. In people with CF, mutations in the CFTR gene can disrupt the normal production or functioning of the CFTR protein found in the cells of the lungs and other parts of the body …

How can I help my child with cystic fibrosis?

How Is Cystic Fibrosis Treated?

  1. get regular exercise.
  2. use an inhaler or nebulizer.
  3. do breathing exercises and cough on purpose.
  4. wear a therapy vest that shakes the chest.
  5. have chest physical therapy (when a parent or trained person bangs gently on the chest or back)

How do you care for a child with cystic fibrosis?

give them time and privacy to perform airway clearance therapy. let them take medication. adjust attendance rules to let them go to medical appointments. provide extensions and help them catch up on lessons and assignments they miss due to medical appointments or illness.

How do you monitor cystic fibrosis?

To diagnose cystic fibrosis, doctors usually perform blood tests. They may test sweat for high salt content, which can indicate cystic fibrosis. If the diagnosis is confirmed, doctors may evaluate the condition with a chest x-ray, chest or abdominal CT or MRI, abdominal ultrasound, or sinus CT.

How is a sweat test done for CF?

In the first part of the test, a colorless, odorless chemical (pilocarpine) and a little electrical stimulation is applied to a small area of the arm or leg to encourage the sweat glands to produce sweat. A person may feel tingling in the area, or a feeling of warmth. This part of the test lasts about five minutes.

What limitations does someone with cystic fibrosis have?

What kind of limitations does someone with CF have? People with CF can live very full, normal lives. There are no limitations to their exercise, diet, or activities. However, due to the different lung infections that they can get, they should not meet or talk with other patients with CF in-person.